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[edit] Discussion

  • Angiomyolipoma (AML) is a benign renal neoplasm composed of fat, vascular, and smooth muscle elements.
  • Incidence of about 0.3-3%.
  • Two types
    • Isolated AML (80%)
      • AML is about 4 times more common in women than in men.
      • Interestingly, 80% of the cases involve the right kidney.
    • AML associated with tuberous sclerosis (20%).
      • AML occurs in 80% patients with tuberous sclerosis.
      • AML also occurs young women with lymphangiomyomatosis without other stigmata of tuberous sclerosis. AML and lymphangiomyomatosis are sometimes considered the forme fruste of tuberous sclerosis.

  • Most small lesions are asymptomatic and incidental findings on images.
  • Complications include hematuria, flank pain, and shock as a result of spontaneous hemorrhage.

[edit] Imaging Findings

Demonstration of fat in renal tumor is virtually diagnostic of AML.

[edit] Images

Patient #1: MRI, CT, and US images demonstrate an angiomyolipoma

Patient #2: Large right angiomyolipoma

[edit] See Also

[edit] External Links

[edit] References