- Biliary hamartomas are also known as biliary microhamartomas or von Meyenburg complex.
- Benign liver malformations consisting of focal disorderly collections of bile ducts, lined with a single layer of low columnar, cuboidal, or flattened epithelium, surrounded by abundant fibrous stroma.
- The bile ducts within the lesions are of varying caliber, ranging from narrow to ectatic.
- May occur as either isolated or multiple lesions.
- These lesions are often discovered incidentally, and if the patient has a primary neoplasm they can be mistaken for metastatic disease.
 Imaging Findings
- Biliary hamartomas are typically multiple round or irregular focal lesions of nearly uniform size (up to 15 mm) scattered throughout the liver.
- Biliary hamartomas are hypoattenuating at CT
- Biliary hamartomas are hypointense at T1-weighted MR imaging and hyperintense at T2-weighted imaging.
- If the echo time is increased at T2-weighted imaging, the signal intensity of these lesions increases further and approaches that of cerebrospinal fluid.
- Biliary hamartomas do not usually show contrast enhancement, although a peripheral enhancing rim has been described. This has been hypothesized as related to compressed surrounding normal liver parenchyma.
Patient #1: Biliary hamartomas
 See Also
 External Links
- Giuseppe Brancatelli, Michael P. Federle, Valérie Vilgrain, Marie-Pierre Vullierme, Daniele Marin, and Roberto Lagalla. Fibropolycystic Liver Disease: CT and MR Imaging Findings. RadioGraphics 2005 25: 659-670.
- Lev-Toaff, AS, Bach, AM, Wechsler, RJ, Hilpert, PL, Gatalica, Z, Rubin, R. The radiologic and pathologic spectrum of biliary hamartomas. Am. J. Roentgenol. 1995 165: 309-313