Congenital lobar emphysema

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[edit] Discussion of Congenital lobar emphysema

  • Congenital lobar emphysema is characterized by progressive overdistention of a lobe.
  • The most commonly affected lobe is the left upper lobe, followed by the right middle lobe.
  • It is more common among males than females.
  • Most patients become symptomatic during the neonatal period, most before 6 months of age
  • Diagnosis is obtained by means of chest radiography and CT, which show hyperinflation of the segment or lobe affected.

[edit] Imaging Findings for Congenital lobar emphysema

  • If the plain radiograph is obtained during the neonatal period, the emphysematous lobe may be opaque and homogeneous because of fetal lung fluid or it may show a diffuse reticular pattern that represents distended lymphatic channels filled with fetal lung fluid.
  • As the fluid is absorbed, the affected segment or lobe becomes hyperlucent, progresing from alveolar opacification to interstitial reticulation to general hyperlucency.
  • Adjacent lobes and structures may be compressed by the emphysematous lobe, and sometimes ipsilateral and contralateral atelectasis may occur.

[edit] Images

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