Cor triatriatum

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[edit] Discussion of Cor triatriatum

  • Cor triatriatum is a rare, congenital anomaly in which a fibromuscular septum subdivides the left atrium into two chambers
  • Associated cardiovascular malformations are common and include atrial septal defect and patent ductus arteriosus.
  • The proximal or accessory chamber lies posterior, usually receiving all of the pulmonary veins.
  • The distal or true left atrial chamber lies anterior, connects to the left atrial appendage, and empties into the left ventricle through the mitral valve.
  • The two atrial chambers communicate through an opening in the subdividing membrane. This opening may be single and stenotic, fenestrated, or quite large.
  • Dyspnea, heart failure and failure to thrive are common clinical findings.

  • The clinical and radiographic pictures depend on the degree of stenosis in the fibromuscular membrane, the integrity of the interatrial septum and on whether or not there are other associated cardiovascular malformations.
  • When cor triatniatum occurs as an isolated defect, the hemodynamic derangement is identical to that of mitral stenosis and the chest radiograph shows a normal sized heart with changes of chronic interstitial edema.

  • Con triatriatum is usually fatal within the first two years of life.
  • The prognosis is related to timely surgical intervention, the degree of obstruction between the two left atria, and the presence or absence of associated anomalies.

[edit] Images

Patient #1

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[edit] References for Cor triatriatum