Prune-belly syndrome

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[edit] Discussion of Prune-belly syndrome

  • AKA Eagle-Barrett syndrome and triad syndrome.
  • Prune-belly syndrome is a specific constellation of anomalies consisting of three major findings associated with a number of other respiratory, gastrointestinal, musculoskeletal, and cardiovascular anomalies.
  1. Lax abdominal wall that results from the absence of rectus muscles.
  2. Bilateral, nonpalpable undescended testes.
  3. Abnormal urinary tract characterized by tortuous, dilated ureters; a megalocystic, dilated prostatic urethra; and renal dysmorphism.

  • Prune-belly syndrome occurs almost exclusively in males, with only occasional female involvement being recorded
  • The condition is of unknown etiology.

[edit] Imaging Findings for Prune-belly syndrome

  • At US, dilated and tortuous ureters with bilateral hydronephrosis are common findings, and kidneys usually show varying degrees of dysplasia and, sometimes, cystic changes.
  • VCUG is used to demonstrate a large, elongated bladder with an irregular contour and bilateral vesicoureteral reflux. A urachal diverticulum is frequently present.

[edit] Images

Patient #1

[edit] External Links

[edit] References for Prune-belly syndrome